In tissues there is a broad distribution of flavin but little is present as free riboflavin. Riboflavin 7 xanthine oxidase xo riboflavin 8 chemistry riboflavin is chemically known as 7,8dimethyl10 1dribityl isoalloxazine. In pure form it is a yelloworange, watersoluble compound. Symptoms may begin from infancy to early adulthood and worsen over time. Accordingly, low intakes of this vitamin have been associated with different diseases, including cancer and cardiovascular diseases. Up to now, these patients are often treated with glucocorticoids as the firstline drug because they are misdiagnosed as polymyositis without muscle. A case of late onset riboflavinresponsive multiple acyl. Department of health and hipoviraminose performance. Handbook of vitamins, fourth edition corneal crosslinking for the treatment of keratoconus. Patient with multiple acylcoa dehydrogenase deficiency.
Scribd is the worlds largest social reading and publishing site. Riboflavin, a component of the b 2 vitaminic complex, plays important roles in biochemistry, especially in redox reactions, due to the ability to participate in both one and twoelectron transfers as well as acting as a photosensitizer. When the condition begins in infancy, the first symptom often is breathing problems, which can be lifethreatening. Riboflavin deficiency definition riboflavin deficiency occurs when the chronic failure to eat sufficient amounts of foods that contain riboflavin produces lesions of the skin, lesions of smooth surfaces in the digestive tract, or nervous disorders. Lateonset multiple acylcoa dehydrogenase deficiency madd is the most common type of lipid storage myopathies in china. Multiple acylcoenzyme a dehydrogenase deficiency madd is an autosomal recessive disorder characterized by mitochondrial electron transfer system defects and impaired fatty acids metabolism. Description riboflavin, also called vitamin b2, is a watersoluble vitamin.
Deficiencia b2 vitaminas nutrientes home nutrifacts. Por lo tanto, es una buena idea tenerlas en su dieta diaria. Acylcoa dehydrogenase deficiency manifesting as recurrent rhabdomyolysis and acute renal failure rumikoizumi 1,naokisuzuki,marinagata1,takafumihasegawa1,yuabe2,yukasaito2, hiroshimochizuki3,makitateyama1 andmasashiaoki1 abstract we report an adult case of lateonset riboflavinresponsive multiple acylcoa dehydrogenase deficiency. B 2 is stable to heat, acid, and oxidation, however. Lipid storage myopathy lsm is a diverse group of lipid metabolic disorders characterized by impaired fatty acids oxidation. Glutathione works to destroy free radicals and detox the liver, as free. Please use one of the following formats to cite this article in your essay, paper or report. Most patients with lateonset madd are well responsive to riboflavin. Riboflavina linus pauling institute oregon state university. Download as ppt, pdf, txt or read online from scribd. The elderly population is particularly at risk for developing vitamin bdeficiency. Riboflavin, vitamin b2, is a watersoluble and heatstable vitamin that. Os seguintes alimentos fornecem riboflavina na dieta.
596 973 1302 389 48 1617 278 1100 1636 78 1529 1316 858 1149 1368 525 191 1280 323 693 1590 209 988 266 815 85 1447 1350 876 1412 479 47 359 1487 547 1293 92